Classic Type Ehlers-Danlos Syndrome with Cutis Laxa-like Histopathologic Findings / 대한피부과학회지
Korean Journal of Dermatology
; : 524-528, 2011.
Article
in Korean
| WPRIM (Western Pacific)
| ID: wpr-148864
Responsible library:
WPRO
ABSTRACT
Ehlers-Danlos syndrome is a connective tissue disorder that is characterized by hyper-extensible skin, hyper-mobile joints, fragile tissues, bleeding diathesis and poor healing of wounds with "cigarette paper" scar formation. Cutis laxa is also a disease of the elastic fibers of the connective tissue and characterized by loose skin folds over all parts of the body, a prematurely aged appearance, a hooked nose with a short colummella and umbilical/inguinal hernias. We report here on two patients who showed the symptoms of Ehlers-Danlos syndrome with histopathologically reduced and distorted elastic fibers, which is usually seen in cutis laxa.
Full text:
Available
Database:
WPRIM (Western Pacific)
Main subject:
Skin
/
Nose
/
Cicatrix
/
Connective Tissue
/
Cutis Laxa
/
Disease Susceptibility
/
Ehlers-Danlos Syndrome
/
Elastic Tissue
/
Hemorrhage
/
Hernia
Type of study:
Diagnostic study
Limits:
Aged
/
Humans
Language:
Korean
Journal:
Korean Journal of Dermatology
Year:
2011
Document type:
Article