A Case of Congenital Onychodysplasia of the Index Fingers Associated with Dandy-Walker Variant / 대한피부과학회지
Korean Journal of Dermatology
; : 959-961, 2006.
Article
in Korean
| WPRIM (Western Pacific)
| ID: wpr-180536
Responsible library:
WPRO
ABSTRACT
Congenital onychodysplasia of the index fingers (COIF) is a rare disorder characterized by various forms of nail dysplasia which are mainly limited to the index fingers. The aetiology of the disease is still a matter of debate. COIF is characterized by five criteria congenital occurrence, unilateral or bilateral index finger involvement, variability of nail appearance, possible hereditary involvement, and frequently associated bone abnormalities. We report a case of COIF, which is associated with Dandy-Walker variant.
Full text:
Available
Database:
WPRIM (Western Pacific)
Main subject:
Dandy-Walker Syndrome
/
Fingers
Language:
Korean
Journal:
Korean Journal of Dermatology
Year:
2006
Document type:
Article