A case of Peutz - Jeghers syndrome with duodenal adenocarcinoma and obstruction / 대한내과학회지
Korean Journal of Medicine
; : 378-382, 1999.
Article
in Korean
| WPRIM (Western Pacific)
| ID: wpr-181241
Responsible library:
WPRO
ABSTRACT
Peutz-Jeghers syndrome is a rare autosomal dominant disorder defined by harmatomatous polyps of the gastrointestinal tracts and the occurrence of melanin spots on the lips(oral mucosa), hands and feet. This syndrome is associated with a variety of gastrointestinal and extraintestinal neoplasms, both benign and malignant. A 28-year old male was admitted to our hospital with abdominal pain and nausea for two months. He had melanin spots involving his lips, buccal mucosa, hands and feet. A small bowel series showed luminal obstruction at the forth portion of the duodenum. And abdominal CT scan showed target-like mass suggesting intussusception on the small bowel. On laparotomy, there was an annular constricting mass adherent to retroperitoneum with metastasis to preaortic lymph nodes. Palliative duodeno-jejunostomy was performed. The histologic finding disclosed signet-ring cell type adenocarcinoma.
Full text:
Available
Database:
WPRIM (Western Pacific)
Main subject:
Phenobarbital
/
Polyps
/
Peutz-Jeghers Syndrome
/
Adenocarcinoma
/
Tomography, X-Ray Computed
/
Abdominal Pain
/
Gastrointestinal Tract
/
Duodenum
/
Foot
/
Hand
Limits:
Adult
/
Humans
/
Male
Language:
Korean
Journal:
Korean Journal of Medicine
Year:
1999
Document type:
Article