Clinical Experience of Malignant Transformation of Multiostotic Fronto-Orbital Fibrous Dysplasia
Journal of the Korean Cleft Palate-Craniofacial Association
; : 87-90, 2006.
Article
in Korean
| WPRIM (Western Pacific)
| ID: wpr-20950
Responsible library:
WPRO
ABSTRACT
The malignant transformation of fibrous dysplasia is a rare condition and the incidence is estimated at 0.4% for fibrous dysplasia and 4% for Albright's syndrome. And fronto-orbital fibrous dysplasia can have a devastating outcome with high rates of recurrence and blindness, especially following incomplete resection. So a radical and extensive approach to treatment is recommended. We report the case of a multiostotic fronto-orbital fibrous dysplasia in a 54-year-old male patient which had a malignant transformation to osteosarcoma. There had been a recurrence after partial removal and no effect by chemotherapy. Although we had have a favorable outcome in functional and aesthetic aspects without any evidences of recurrence by total removal and reconstruction with titanium mesh, the patient died with lung metastasis 4 and half years later after the first operation.
Full text:
Available
Database:
WPRIM (Western Pacific)
Main subject:
Recurrence
/
Titanium
/
Osteosarcoma
/
Blindness
/
Incidence
/
Drug Therapy
/
Fibrous Dysplasia, Polyostotic
/
Lung
/
Neoplasm Metastasis
Type of study:
Incidence study
/
Prognostic study
Limits:
Humans
/
Male
Language:
Korean
Journal:
Journal of the Korean Cleft Palate-Craniofacial Association
Year:
2006
Document type:
Article