Congenital Aniridia

ABSTRACT

Aniridia is a very rare disorder the main features of which are congenitally partial or nearly complete absence of the iris and foveal hypoplasia. The authors obseved aniridia in two generations, mother and one daughter. They have cataract, ectopia lentis, nystagmus and foveal hypoplasia as well as aniridia. The lens of daughter was aspirated in both eyes consecutively. Her final best corrected visual acuity was 0.3 with +sph. 13.00D in each eyes.