Primary intestinal lymphangiectasia in children / 中华实用儿科临床杂志

ABSTRACT

With the progress of clinical understanding and examination methods,the incidence of primary intestinal lymphangiectasia in children is gradually increased,congenital lymphatic malformation is the most common pathogen,protein-losing enteropathy is the main clinical feature.In addition to endoscopic and histologic examination,lymphatic radionuclide imaging,has become the common method in diagnosis,especially suitable for infants and young children.The management of lymphangiectasia includea low-fat diet associated with supplementary medium chain three acyl glycerol,symptomatic treatment,medicine and surgery.Emphasis should be put on long-term management and follow-up work.