A Case of Lymphangioleiomyomatosis Presenting as a Lung Mass / 결핵및호흡기질환
Tuberculosis and Respiratory Diseases
; : 289-293, 2007.
Article
in Korean
| WPRIM (Western Pacific)
| ID: wpr-73581
Responsible library:
WPRO
ABSTRACT
Lymphangioleiomyomatosis (LAM) is a rare disease that affects females of reproductive age. It is characterized by the abnormal proliferation of smooth muscle cells in the lung and along the axial lymphatics. We report a case of lymphangioleiomyomatosis presenting as a lung mass. The patient visited the emergency room because of dyspnea upon exertion. The chest X-ray showed a lung mass in the right lower lung field and a pneumothorax in the left lung. Chest computed tomography revealed a 5 x 3 cm sized mass in the right lower lobe and multiple thin-walled small cysts scattered in both lungs. Transbronchial biopsy of the lung mass was performed. The biopsy specimen showed atypical smooth muscle cell proliferation and cystic dilatation of the terminal bronchioles, which confirmed the diagnosis of lymphangioleiomyomatosis. To the best of our knowledge, this is the first case of lymphangioleiomyomatosis presenting as a lung mass.
Full text:
Available
Database:
WPRIM (Western Pacific)
Main subject:
Pneumothorax
/
Thorax
/
Biopsy
/
Lymphangioleiomyomatosis
/
Myocytes, Smooth Muscle
/
Rare Diseases
/
Diagnosis
/
Dilatation
/
Dyspnea
/
Emergency Service, Hospital
Type of study:
Diagnostic study
Limits:
Female
/
Humans
Language:
Korean
Journal:
Tuberculosis and Respiratory Diseases
Year:
2007
Document type:
Article