Progress in managing pulmonary arterial hypertension associated with congenital heart disease / 中华实用儿科临床杂志

ABSTRACT

Pulmonary arterial hypertension(PAH)is the most common complication of congenital heart disease (CHD). Because of the complexity and diversity of cardiac anatomy and pathophysiology,as well as a variety of adap-tive mechanisms that are not fully understood,little attention is paid on pulmonary arterial hypertension associated with congenital heart disease(CHD-PAH). This article aims to summarize the clinical status,disease characteristics,out-comes,and prognosis of CHD -PAH in Pediatric Cardiology,Beijing Anzhen Hospital,proposing current unresolved issues and future challenges.