CT imaging features of hepatic perivascular epithelioid cell tumor / 实用放射学杂志

ABSTRACT

Objective To investigate the CT feasures of hepatic perivascular epithelioid cell tumors (PEComa),to improve the understanding and diagnosis of this disease.Methods CT findings and clinical data of 13 patients with hepatic PEComa were analyzed retrospectively.Results Among the 1 3 PEComa patients,2 cases were multiple focis and 1 1 cases were single lesion.The maximum diameter of the lesions ranges from 26 mm to 96 mm,with mean diameter (52.77±24.94)mm.The density of 6 cases large lesions was heterogeneous on plain CT image,and the atery phase showed significantly inhomogeneous enhancement and the enhancement decreased in venous phase.7 cases of small lesions was homogeneous in density and showed uniform enhancement in arterial phase.The adjacent organs were compressed in 4 cases,the hepatic artery was located at the margin or inside the tumor in 4 cases,the portal vein or its branch passed through the tumor in 2 cases,and the inferior vena cava was compressed and shifted in 1 case.Conclusion CT manifestations of hepatic PEComa have some characteristics,when the tumor shows homogeneous in density and uniform enhancement in arterial phase,and the enhancement decreases in venous phase,with the thick vessel in the center or at the peripheral,it may prompt diagnosis.