A Case of Pneumatosis Cystoides Intestinalis in a Patient with Systemic Lupus Erythematosus / 대한내과학회지
Korean Journal of Medicine
; : 283-286, 2012.
Article
in Korean
| WPRIM (Western Pacific)
| ID: wpr-96827
Responsible library:
WPRO
ABSTRACT
Pneumatosis cystoides intestinalis, which is characterized by multiple air-filled cysts in the intestinal mucosa, submucosa, and subserosa, is associated with autoimmune disorders, including systemic sclerosis, inflammatory myopathy and, rarely, systemic lupus erythematosus (SLE). Here, we report the case of a 57-year-old female with a 2-year history of SLE who developed pneumatosis cystoides intestinalis. The patient's symptoms were improved with conservative management. Although pneumatosis cystoides intestinalis is an uncommon manifestation of SLE, and follows a mainly benign course, it can be associated with vasculitis, which has a poor prognosis.
Full text:
Available
Database:
WPRIM (Western Pacific)
Main subject:
Pneumatosis Cystoides Intestinalis
/
Prognosis
/
Scleroderma, Systemic
/
Vasculitis
/
Prednisolone
/
Intestinal Mucosa
/
Lupus Erythematosus, Systemic
/
Myositis
Type of study:
Prognostic study
Limits:
Female
/
Humans
Language:
Korean
Journal:
Korean Journal of Medicine
Year:
2012
Document type:
Article