Transcatheter closure of rare type Ⅱ Abernethy malformation with pulmonary hypertension in children: A case report / 临床肝胆病杂志
Journal of Clinical Hepatology
; (12): 2663-2667, 2023.
Article
in Chinese
| WPRIM (Western Pacific)
| ID: wpr-998824
Responsible library:
WPRO
ABSTRACT
Abernethy malformation, also known as congenital portosystemic shunts, is rare in clinical practice, with less than 300 cases reported in the global literature up to 2019. The disease can have serious complications such as pulmonary hypertension, liver tumor, and liver failure and tends to have an extremely poor prognosis, and early diagnosis and active and effective treatment can reduce and delay the onset of complications. In this case, portography combined with balloon occlusion helped to display the underdeveloped slender portal vein with dysplasia, so that the child who was formerly misdiagnosed with type Ⅰ Abernethy malformation was diagnosed with type Ⅱ Abernethy malformation, and then the child was successfully treated by transcatheter closure. This article gives a detailed report of this case.
Full text:
Available
Database:
WPRIM (Western Pacific)
Language:
Chinese
Journal:
Journal of Clinical Hepatology
Year:
2023
Document type:
Article