[Partial nodular transformation of the liver with portal hypertension. A new case. Review of the literature]. / Transformation nodulaire partielle du foie avec hypertension portale. Une nouvelle observation. Revue de la littérature.

Based on a case of partial nodular transformation of the liver (PNT) with portal hypertension and splenic microaneurysms in a 24 year old man, the authors review the literature on this subject which only consists of 7 female cases. The authors point out the rarity of this entity which, together with hyperplastic nodular regeneration, is one of the causes of the essential portal hypertension syndrome. They stress the early onset of this disease (mean age of 35 years), on the severity of its clinical course and on the surgical possibilities of porto-caval shunts. The pathogenesis of PNT remains unknown.