Perioperative administration of recombinant activated factor VII in a Glanzmann's thrombasthenia patient with platelet refractoriness: case report
Braz. J. Anesth. (Impr.)
; 72(6): 823-825, Nov.-Dec. 2022.
Article
em En
| LILACS
| ID: biblio-1420620
Biblioteca responsável:
BR891.2
ABSTRACT
Abstract Glanzmannʼs Trombasthenia (GT) is a genetic disorder, that develops with a tendency toward bleeding and is characterized by the absence or decrease in platelet aggregation. Surgical bleeding may be difficult to control. Platelet transfusion is the main treatment, albeit refractoriness can occur. We describe the case of a patient with GT and platelet refractoriness, who was submitted to radical prostatectomy and dental extraction. The perioperative treatment with apheresis platelet concentrate and activated recombinant factor seven allowed the procedures to be performed uneventfully. We discuss the complexity of the case and the treatment option.
Palavras-chave
Texto completo:
1
Coleções:
01-internacional
Base de dados:
LILACS
Assunto principal:
Trombastenia
Limite:
Humans
/
Male
Idioma:
En
Revista:
Braz J Anesthesiol
/
Braz. J. Anesth. (Impr.)
/
Brazilian Journal of Anesthesiology (Impresso)
/
Brazilian journal of anesthesiology (English edition. Online)
Assunto da revista:
ANESTESIOLOGIA
Ano de publicação:
2022
Tipo de documento:
Article
País de afiliação:
Brasil
País de publicação:
Brasil