Case for diagnosis. Systemic light chain amyloidosis with cutaneous involvement
An. bras. dermatol
; An. bras. dermatol;92(5): 731-732, Sept.-Oct. 2017. graf
Article
em En
| LILACS
| ID: biblio-887036
Biblioteca responsável:
BR1.1
ABSTRACT
Abstract Systemic light chain amiloydosis is a rare disease. Due to its typical cutaneous lesions, dermatologists play an essential role in its diagnosis. Clinical manifestations vary according to the affected organ and are often unspecific. Definitive diagnosis is achieved through biopsy. We report a patient with palpebral amyloidosis, typical bilateral ecchymoses and cardiac involvement, without plasma cell dyscrasia or lymphomas. The patient died shortly after the diagnosis.
Palavras-chave
Texto completo:
1
Coleções:
01-internacional
Base de dados:
LILACS
Assunto principal:
Dermatopatias
/
Amiloidose de Cadeia Leve de Imunoglobulina
Tipo de estudo:
Diagnostic_studies
Limite:
Adult
/
Female
/
Humans
Idioma:
En
Revista:
An. bras. dermatol
Assunto da revista:
DERMATOLOGIA
Ano de publicação:
2017
Tipo de documento:
Article
País de afiliação:
Brasil
País de publicação:
Brasil