Achados cardíacos em 31 pacientes com síndrome de Noonan / Cardiac findings in 31 patients with Noonan's syndrome
Arq. bras. cardiol
; Arq. bras. cardiol;75(5): 405-12, Nov. 2000.
Article
em Pt, En
| LILACS
| ID: lil-273496
Biblioteca responsável:
BR1.1
ABSTRACT
OBJECTIVE:
To evaluate cardiac findings in 31 Noonan syndrome patients.METHODS:
Thirty-one (18 males and 13 females)patients from 26 families affected with Noonan's syndrome were evaluated from the cardiac point of view with electrocardiography and echodopplercardiography.RESULTS:
Twenty patients had some type of cardiac abnormality. The most frequent was pulmonary valve stenosis followed by hypertrophic myocardiopathy, commonly associated with valve defects. Upper deviation of the QRS axis was observed in 80 percent of these patients.CONCLUSION:
In view of the high frequency and diversity of cardiac abnormalities present in Noonan syndrome, cardiac evaluation with electrocardiography and echocardiography should be performed in all patients diagnostically suspected of having this disease
Texto completo:
1
Coleções:
01-internacional
Base de dados:
LILACS
Assunto principal:
Doenças Cardiovasculares
/
Síndrome de Noonan
Tipo de estudo:
Diagnostic_studies
Limite:
Adolescent
/
Adult
/
Child
/
Child, preschool
/
Female
/
Humans
/
Infant
/
Male
Idioma:
En
/
Pt
Revista:
Arq Bras Cardiol
/
Arq. bras. cardiol
/
Arq. bras. cardiol. (Online)
/
Arquivos brasileiros de cardiologia (Impresso)
Assunto da revista:
CARDIOLOGIA
Ano de publicação:
2000
Tipo de documento:
Article
País de afiliação:
Brasil
País de publicação:
Brasil