Angiosarcoma in a 3-year-old child with congenital lymphedema
Appl. cancer res
; 29(4): 188-191, Oct.-Dec. 2009. ilus, tab
Article
em En
| LILACS, Inca
| ID: lil-547653
Biblioteca responsável:
BR30.1
ABSTRACT
Angiosarcoma occurring in chronic lymphedema has been described in more than 200 cases, especially in the upper extremity following radical mastectomy (Stewart-Treves syndrome). However, angiosarcoma developing in congenital lymphedema is quite rare and the literature presents only 14 cases. Our patient is a girl with congenital lymphedema of the left lower limb that developed an angiosarcoma at 3 years of age, noted initially as a painful nodular lesion on the left thigh. This seems to be the earliest presentation of angiosarcoma associated with lymphedema. It claims attention to a careful evaluation of any lesions in a child with lymphedema to provide a better prognosis, which is allowed by precocious diagnosis and rapid interventions.
Texto completo:
1
Coleções:
01-internacional
Base de dados:
LILACS
/
Inca
Assunto principal:
Sarcoma
/
Extremidade Superior
/
Hemangiossarcoma
/
Linfedema
Tipo de estudo:
Prognostic_studies
Limite:
Child
Idioma:
En
Revista:
Appl. cancer res
Assunto da revista:
NEOPLASIAS
Ano de publicação:
2009
Tipo de documento:
Article
País de afiliação:
Brasil
País de publicação:
Brasil