Transnodal lymphangiography and post-CT for protein-losing enteropathy in Noonan syndrome.
Minim Invasive Ther Allied Technol
; 24(4): 246-9, 2015.
Article
em En
| MEDLINE
| ID: mdl-25636017
Noonan syndrome, which is a multiple congenital disorder, may be associated with lymphatic abnormalities. Protein-losing enteropathy (PLE) developing in Noonan syndrome is rare. We performed transnodal lymphangiography by directly accessing bilateral inguinal nodes under ultrasound guidance in a 17-year-old female with PLE developing in Noonan syndrome to assess detailed anatomical findings regarding lymphatic vessels. There have been no reports on transnodal lymphangiography for Noonan syndrome. Post-lymphangiographic CT images revealed multiple lymphatic abnormalities and lipiodol extravasation into the duodenum and the proximal jejunum. Transnodal lymphangiography was easy and safe for PLE developing in Noonan syndrome, and post-lymphangiographic CT provided invaluable information.
Palavras-chave
Texto completo:
1
Coleções:
01-internacional
Base de dados:
MEDLINE
Assunto principal:
Enteropatias Perdedoras de Proteínas
/
Linfografia
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Tomografia Computadorizada por Raios X
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Síndrome de Noonan
Limite:
Adolescent
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Female
/
Humans
Idioma:
En
Revista:
Minim Invasive Ther Allied Technol
Assunto da revista:
TERAPEUTICA
Ano de publicação:
2015
Tipo de documento:
Article
País de afiliação:
Japão
País de publicação:
Reino Unido