Uterine didelphys with transverse vaginal septum in a 16-year-old female: the third case report in the medical literature.

ABSTRACT

Müllerian duct anomalies (MDAs) are congenital disorders of the female genital tract resulting from abnormal embryological development of the Müllerian ducts. These abnormalities occur in approximately 0.5%-5.0% of the general population. The case involves a 16-year-old Middle Eastern female referred to the clinic due to primary amenorrhea and lower abdominal pain. Upon evaluation, we identified a congenital anomaly known as uterine didelphys with a transverse vaginal septum. Uterine didelphys is a type of Müllerian duct anomaly characterized by the complete duplication of the uterus, cervix, and sometimes the vagina. Our case is exceptional, as most reported instances feature a longitudinal vaginal septum with uterine didelphys, and it is rare to find both longitudinal and transverse vaginal septa. The combination of uterine didelphys with only a transverse vaginal septum is extremely rare. To the best of our knowledge, this is only the third reported case of its kind.