Primary infantile haemangioendothelioma of the liver

ABSTRACT

A three-week-old female infant who was admitted to the University Hospital of the West Indies in severe congestive cardiac failure developed haematological abnormalities and died two days later. At autopsy, she was found to have multicentric haemangioendotheliomas of the liver. Intractable cardiac failure and haematological abnormalities are typical manifestations of this infantile vascular tumour of the liver which may obscure the diagnosis (AU)