Mycobacterium abscessus Lung Disease in a Patient with Kartagener Syndrome / 결핵및호흡기질환
Tuberculosis and Respiratory Diseases
; : 136-140, 2014.
Article
em En
| WPRIM
| ID: wpr-103198
Biblioteca responsável:
WPRO
ABSTRACT
Primary ciliary dyskinesia (PCD) is characterized by the congenital impairment of mucociliary clearance. When accompanied by situs inversus, chronic sinusitis and bronchiectasis, PCD is known as Kartagener syndrome. The main consequence of impaired ciliary function is a reduced mucus clearance from the lungs, and susceptibility to chronic respiratory infections due to opportunistic pathogens, including nontuberculous mycobacteria (NTM). There has been no report of NTM lung disease combined with Kartagener syndrome in Korea. Here, we report an adult patient with Kartagener syndrome complicated with Mycobacterium abscessus lung disease. A 37-year-old female presented to our hospital with chronic cough and sputum. She was ultimately diagnosed with M. abscessus lung disease and Kartagener syndrome. M. abscessus was repeatedly isolated from sputum specimens collected from the patient, despite prolonged antibiotic treatment. The patient's condition improved and negative sputum culture conversion was achieved after sequential bilateral pulmonary resection.
Palavras-chave
Texto completo:
1
Base de dados:
WPRIM
Assunto principal:
Infecções Respiratórias
/
Sinusite
/
Situs Inversus
/
Escarro
/
Bronquiectasia
/
Depuração Mucociliar
/
Síndrome de Kartagener
/
Tosse
/
Coreia (Geográfico)
/
Pulmão
Limite:
Adult
/
Female
/
Humans
País/Região como assunto:
Asia
Idioma:
En
Revista:
Tuberculosis and Respiratory Diseases
Ano de publicação:
2014
Tipo de documento:
Article