Acquired Hepatocerebral Degeneration Presenting with Downbeat Nystagmus and Ataxia: A Case Report
Journal of the Korean Neurological Association
; : 101-104, 2007.
Artigo
em Coreano
| WPRIM (Pacífico Ocidental)
| ID: wpr-107151
Biblioteca responsável:
WPRO
ABSTRACT
Nystagmus or ataxia is a rare manifestation of acquired hepatocerebral degeneration (AHCD). A 49-year-old woman presented with downbeat nystagmus and limb and gait ataxia. She was diagnosed as primary biliary cirrhosis with a gastric varix. Brain MRI showed cerebellar vermian atrophy and characteristic T1 high-signal intensities in bilateral globus pallidi and ventral midbrain. We report a rare case of AHCD manifesting prominent cerebellar symptoms. This has not yet been reported in Korea.
Texto completo:
Disponível
Base de dados:
WPRIM (Pacífico Ocidental)
Assunto principal:
Ataxia
/
Atrofia
/
Encéfalo
/
Mesencéfalo
/
Imageamento por Ressonância Magnética
/
Varizes Esofágicas e Gástricas
/
Marcha Atáxica
/
Extremidades
/
Degeneração Hepatolenticular
/
Coreia (Geográfico)
Limite:
Feminino
/
Humanos
País/Região como assunto:
Ásia
Idioma:
Coreano
Revista:
Journal of the Korean Neurological Association
Ano de publicação:
2007
Tipo de documento:
Artigo