A Case of Congenital Disseminated Malignant Rhabdoid Tumor of the Soft Tissue in Neonate / 대한주산의학회잡지
Korean Journal of Perinatology
; : 311-316, 2010.
Artigo
em Coreano
| WPRIM (Pacífico Ocidental)
| ID: wpr-130993
Biblioteca responsável:
WPRO
ABSTRACT
Malignant rhabdoid tumor (MRT) was first described as a "rhabdomyosarcomatoid" variant of Wilms tumor, but was later identified as a distinct entity. MRTs are extremely rare and highly aggressive neoplasm with poor outcome, occurring mostly in kidneys and central nervous system, less frequently in extrarenal sites. MRTs are referred to as "congenital" when it is diagnosed at or immediately after birth. There are few reports about congenital disseminated MRT at birth. We report a case of congenital malignant rhabdoid tumor presenting as a soft tissue mass in the right arm at birth although the autopsy revealed the systemic disseminated tumors through the whole body with typical microscopic findings.
Texto completo:
Disponível
Base de dados:
WPRIM (Pacífico Ocidental)
Assunto principal:
Braço
/
Autopsia
/
Sistema Nervoso Central
/
Tumor Rabdoide
/
Tumor de Wilms
/
Parto
/
Rim
Tipo de estudo:
Estudo prognóstico
Limite:
Humanos
/
Recém-Nascido
Idioma:
Coreano
Revista:
Korean Journal of Perinatology
Ano de publicação:
2010
Tipo de documento:
Artigo