IgG4-Related Systemic Disease Can Be Easily Mistaken as a Uroepithelial Tumor / 전남의대학술지
Chonnam Medical Journal
; : 39-42, 2015.
Article
em En
| WPRIM
| ID: wpr-133646
Biblioteca responsável:
WPRO
ABSTRACT
Immunoglobulin G4-related disease (IgG4-RD) is a newly recognized systemic syndrome characterized by elevated serum IgG4 concentrations and tumefaction or tissue infiltration by IgG4-positive plasma cells. We experienced a case of IgG4-RD involving multiple organs in a 64-year-old female who was referred for a suspected uroepithelial tumor. A mass biopsy confirmed dense lymphoplasmacytic infiltration with an increased number of IgG4-positive plasma cells. We discuss this case and review the literature to bring IgG4-RD to the attention to clinicians because it responds dramatically well to steroid therapy and should be kept in mind as a differential diagnosis to avoid unnecessary surgery.
Palavras-chave
Texto completo:
1
Base de dados:
WPRIM
Assunto principal:
Plasmócitos
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Esclerose
/
Biópsia
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Imunoglobulina G
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Imunoglobulinas
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Procedimentos Desnecessários
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Diagnóstico Diferencial
/
Rim
Tipo de estudo:
Diagnostic_studies
Limite:
Female
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Humans
Idioma:
En
Revista:
Chonnam Medical Journal
Ano de publicação:
2015
Tipo de documento:
Article