A Case of Omphalocele-Exstrophy-Imperforate Anus-Spinal Defects(OEIS syndrome)
Journal of the Korean Pediatric Society
; : 1386-1389, 2000.
Artigo
em Coreano
| WPRIM (Pacífico Ocidental)
| ID: wpr-141708
Biblioteca responsável:
WPRO
ABSTRACT
Omphalocele-exstrophy-imperforate anus-spinal defects(OEIS Syndrome) is a single defect in early mesoderm, and its incidence is about one in 250,000. If was first described by Littre in 1709. The characteristics of this disorder is omphalocele, extrpohy of bladder, imperforate anus and spina bifida. There have been reports of longtime survival made possible by several operations, but for most cases normal life is impossible due to the deformities. We report a case of OEIS complex who had omphalocele, exstrophy of bladder, imperforate anus and spina bifida from birth.
Texto completo:
Disponível
Base de dados:
WPRIM (Pacífico Ocidental)
Assunto principal:
Anus Imperfurado
/
Anormalidades Congênitas
/
Bexiga Urinária
/
Incidência
/
Disrafismo Espinal
/
Extrofia Vesical
/
Parto
/
Hérnia Umbilical
/
Mesoderma
Tipo de estudo:
Estudo de incidência
/
Estudo prognóstico
Idioma:
Coreano
Revista:
Journal of the Korean Pediatric Society
Ano de publicação:
2000
Tipo de documento:
Artigo