A Case of Cowden Syndrome / 대한피부과학회지
Korean Journal of Dermatology
; : 829-831, 2007.
Article
em Ko
| WPRIM
| ID: wpr-17650
Biblioteca responsável:
WPRO
ABSTRACT
Cowden syndrome is a rare autosomal dominant disorder characterized by mucocutaneous alterations including multiple facial trichilemmomas, oral mucosal papillomatosis, and acral keratoses. Extracutaneous lesions include polyposis of the gastrointestinal tract, and other multiple hamartoma of the internal organs. A 39 year-old man presented with multiple verruca-like papules and lichenified patches on the face, one year ago. He had been treated for atopic dermatitis for more than 10 years. Although he had been treated in accordance with atopic dermatitis for 1 year, his skin lesions had not improved, so a skin biopsy was performed. The skin biopsy specimen revealed the typical finding of trichilemmoma. Colonoscopy diagnosed diffuse colorectal polyposis. The clinical and hisopathologic findings were consistent with Cowden syndrome. We, herein, report a case of Cowden syndrome with atopic dermatitis.
Palavras-chave
Texto completo:
1
Base de dados:
WPRIM
Assunto principal:
Papiloma
/
Pele
/
Biópsia
/
Síndrome do Hamartoma Múltiplo
/
Colonoscopia
/
Trato Gastrointestinal
/
Dermatite Atópica
/
Hamartoma
/
Ceratose
Limite:
Adult
/
Humans
Idioma:
Ko
Revista:
Korean Journal of Dermatology
Ano de publicação:
2007
Tipo de documento:
Article