Anesthetic managements for correction of aortic valve regurgitation in a patient with Loeys-Dietz Syndrome: A case report / 대한마취과학회지
Korean Journal of Anesthesiology
; : 371-375, 2009.
Article
em Ko
| WPRIM
| ID: wpr-189216
Biblioteca responsável:
WPRO
ABSTRACT
Loeys-Dietz Syndrome (LDS) is a recently described autosomal dominant aortic aneurysm syndrome with widespread systemic involvement. It is characterized by the triad of 1) arterial tortuosity and aneurysms, 2) hypertelorism, and 3) bifid uvula or cleft palate. A 12-year-old boy with LDS was scheduled to undergo correction of aortic valve regurgitation due to aortic annuloectasia. We report our clinical experiences of a case of LDS patient with brief review of related literatures and relevant anesthetic problems.
Palavras-chave
Texto completo:
1
Base de dados:
WPRIM
Assunto principal:
Aneurisma Aórtico
/
Valva Aórtica
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Artérias
/
Dermatopatias Genéticas
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Úvula
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Fissura Palatina
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Malformações Vasculares
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Síndrome de Loeys-Dietz
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Hipertelorismo
/
Instabilidade Articular
Limite:
Child
/
Humans
Idioma:
Ko
Revista:
Korean Journal of Anesthesiology
Ano de publicação:
2009
Tipo de documento:
Article