Macrophage Activation Syndrome as the Extreme Form of Kawasaki Disease / 소아감염
Korean Journal of Pediatric Infectious Diseases
; : 177-181, 2010.
Article
em Ko
| WPRIM
| ID: wpr-219039
Biblioteca responsável:
WPRO
ABSTRACT
Few cases of macrophage activation syndrome (MAS) or reactive hemophagocytic lymphohistiocytosis (HLH) during the acute febrile phase of Kawasaki disease (KD) have been reported. We report on a case of a 19 month-old girl with MAS or reactive HLH during the course of KD. Despite immunoglobulin and steroid therapy, she showed persistent fever with hepatosplenomegaly and evidence of hemophagocytosis in the bone marrow. A high index of suspicion for clinical features associated with MAS is necessary for KD patients in order to provide appropriate treatment.
Palavras-chave
Texto completo:
1
Base de dados:
WPRIM
Assunto principal:
Compostos Orgânicos
/
Medula Óssea
/
Imunoglobulinas
/
Linfo-Histiocitose Hemofagocítica
/
Síndrome de Ativação Macrofágica
/
Febre
/
Ativação de Macrófagos
/
Macrófagos
/
Síndrome de Linfonodos Mucocutâneos
Limite:
Humans
Idioma:
Ko
Revista:
Korean Journal of Pediatric Infectious Diseases
Ano de publicação:
2010
Tipo de documento:
Article