A Case of Successful Surgical Treatment for Acute Type A Aortic Dissection in Late Pregnancy with Marfan Syndrome / 日本心臓血管外科学会雑誌

ABSTRACT

We report a case of successful surgical treatment for acute aortic dissection in a patient with late pregnancy with Marfan syndrome. The patient was a 32-year-old primipara. She experienced sudden precordial pain and visited on other hospital at 29 weeks' gestation. She was given a diagnosis of acute type A aortic dissection on computed tomography (CT), and was referred to our hospital for surgery. The earliest possible operation was required, but, in view of the risk of massive bleeding following placental separation due to heparin administration for cardiopulmonary bypass, Caesarian section and abdominal total hysterectomy were initially performed, followed 2 days later by the Bentall procedure plus prosthetic graft replacement of the ascending aorta and aortic arch in a two-stage operation. The postoperative course of the mother and infant was uneventful. The treatment strategy for Marfan syndrome complicated by aortic dissection in late pregnancy is very important. We were able to safely perform surgery and perioperative management using a two-stage operation, that is, by performing Caesarian section first, then strictly controlling circulatory dynamics under sedation and artificial ventilation in the ICU, and subsequently performing repair of the heart and aorta after the subsidence of obstetric hemorrhage.