Congenital pulmonary vein atresia / 中华实用儿科临床杂志
Chinese Journal of Applied Clinical Pediatrics
; (24): 1207-1210, 2014.
Artigo
em Chinês
| WPRIM (Pacífico Ocidental)
| ID: wpr-453738
Biblioteca responsável:
WPRO
ABSTRACT
Congenital pulmonary vein atresia (PVA) is a rare anomaly in clinic.Patients with congenital PVA are usually symptomatic and present with recurrent episodes of pneumonia or haemoptysis in infancy or childhood.Because PVA often occurs in the setting of other congenital heart lesions,so repeated infection of lung might be considered to associate with left-to-right intracardiac shunt with increased pulmonary blood,but ignore further examination of more rare cause.Diagnosis of PVA is based primarily on imaging test,chest radiograph,lung CT and fiberoptic bronchoscopy might reveal some indirect characteristic changes of the disease.Three dimensional contrast enhanced cardiac CT can make a definite diagnosis.The disease is difficult to cure at present,the aim of the treatment is to preserve lung function.The prognosis is associated with the number of involved pulmonary veins.
Texto completo:
Disponível
Base de dados:
WPRIM (Pacífico Ocidental)
Tipo de estudo:
Estudo prognóstico
Idioma:
Chinês
Revista:
Chinese Journal of Applied Clinical Pediatrics
Ano de publicação:
2014
Tipo de documento:
Artigo