Congenital Mastoid Cholesteatoma Presenting as a Mass

ABSTRACT

Cholesteatoma is one of the common disorders encountered by the otorhinolaryngologist. However, there are few cases with an atypical clinical presentation and computed tomography scan findings which make cholesteatoma difficult to diagnose. We report a rare case of congenital mastoid cholesteatoma that presented as a mass obstructing the external auditory canal. The disease was successfully treated with a mastoidectomy and histopathological examination confirmed the diagnosis of cholesteatoma. Clinicians should consider congenital mastoid cholesteatoma in the differential diagnosis of patients with a mass in the external auditory canal. The diagnosis is likely to be made based on surgical and histopathological findings.