The Report of macrophage activation syndrome in 9 children / 中华风湿病学杂志
Chinese Journal of Rheumatology
; (12)2000.
Article
em Zh
| WPRIM
| ID: wpr-683143
Biblioteca responsável:
WPRO
ABSTRACT
Objective To analyze the clinical characteristics of macrophage activation syndrome (MAS). Methods Clinical data was analyzed in 9 children who had been diagnosed as MAS in our hospital from Jan, 2003 to Aug, 2006. Results Seven children were boys, 2 children were girls, aged 5 months to 12 years. Clinical manifestations included long-term fever, hemophagocytic cell in bone marrow, anemia, arthritis, enlargement of lymph nodes, enlargement of liver and spleen, liver dysfunction, abnormal fat metabolism. Two cases had acute respiratory, distress syndrome(ARDS), 2 cases were complicated with multi- pie organ failure(MOF), two patients died. Glucocorticoid combined with immunosuppressive therapy were effective, HP(Plasma Exchange)was applied in one severe case and was shown to he effective. Conclusion MAS is a serious complication of JIA, especially in systemic-onset juvenile idiopathic arthritis. It is very im- portant to recognize and treat MAS earlier.
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Base de dados:
WPRIM
Idioma:
Zh
Revista:
Chinese Journal of Rheumatology
Ano de publicação:
2000
Tipo de documento:
Article