A Case of Pseudomyogenic Hemangioendothelioma of the Lower Extremity
Annals of Dermatology
; : 426-429, 2020.
Article
| WPRIM
| ID: wpr-831459
Biblioteca responsável:
WPRO
ABSTRACT
Pseudomyogenic hemangioendothelioma (PMH) is a rare vascular tumor and was recently recognized as a distinct entity. It has a predilection for young male adults and it frequently occurs in distal extremities. Although it is known to follow an indolent course, multi-focal presentation and local recurrence are common. PMH should be differentiated from epithelioid sarcoma, epithelioid hemangioendothelioma, dermatofibrosarcoma protuberans, and rhabdomyosarcoma. Its characteristic immunohistochemical staining pattern and recurrent translocation t(7:19)(q22:q13) are the basis for its diagnosis. Surgical excision is the mainstay treatment, although chemotherapy can be considered in non-operable patients. We present a rare case of a 40-year-old Korean male patient diagnosed with PMH through an excisional biopsy to facilitate the recognition PMH in the clinical practice.
Texto completo:
1
Base de dados:
WPRIM
Revista:
Annals of Dermatology
Ano de publicação:
2020
Tipo de documento:
Article