La nephroblastomatose: a propos de deux cas

Rare entity recently individualized, Nephroblastomatosis refers to the finding of accumulations of metanephric blastema in infants and children at any time beyond 36 weeks gestation or in an abnormal location or quantity in younger infants. Two subtypes: -Multifocal superficial Nephroblastomatosis; -Diffuse Nephroblastomatosis Malformations associated could lead to emphasize the hypothesis of genetical abnormality. It may be confused with bilateral Nephroblastoma. Our purpose will be to describe the clinical, radiological, pathological features and the prognosis of Nephroblastomatis in one hand, and in the other hand the close embryogenic and encogenic relationship between Nephroblastoma and Nephroblastomatosia

L'atresie antro-pylorique: a props d'une observation

We report here a moroccan antro-pyloric atresia case. This malformation constitutes an uncommon affection seeing that there are Only 96 cases reported in literature. The obstacle is more often a consequence of a diaphragme. Sometimes, the stomach and the duodenum are completely separated. In the other cases, they are joined by a fibrous cord. The symptoms are very typical. They include non-bilious earlier vomitings with on X-Ray a single gaseous or hydro-aeric image in the stomach without any air in the remainder of the intestine. When the atresia isn't immediately show at surgery, the radiological signs induce to explore the pylorus by using a probe performed from incisions in the prepyloric and duodenal region. This latter is able to detect the fibrous cord and a web which are most frequent.The treatment depends on the anatomical form of the malformation. It can be either a diaphram excision with a pyloroplastiey or pyloroplasty anastomosis or gastrojejunal anastomosis in the presence of a continuity solution or a fibrous cord between the stomach and the first duodenum

Les duplications gastriques: a propos de deux observations

From our study of the gastric duplications, it result that they are cystic or tubular formations which can communicate with the gastric lumen and their detection often is in infancy. We noted a female prevalence two cases for one male case. The clinical signs which are the most frequently encountered are vomotings, abdominal mass palpation, abdominal pains and, unfrequently a weight loss, an anemia and digestive hemorrhages We frequently find co-existent malformations which essentially are digestive malformations on one hand and vertebral on the other hand The complications increase according the patient's age. they essentially include ulcerations of duplications wall with or without perforation and ulcerations of digestive duct leading to digestive hemorrhanges. The differential diagnosis concerns the real congenital diverticula of the stomach and all the abdominal tumors.we reported the different etio-embryologic theories. They are numerous and no one is completely satisfying. Nevertheless, we think that the "SPLIT NOTOCHORD'S SYNDROM" is the most tempting. Our two gastric Duplications, managed Child Surgery of Rabat U.H.C. during the last years, present clinical, radiological an therapeutic signs which are the most frequently reported literature. Lastly, to recognize a gastric Duplication isn't at the present time an exceptional diagnosis. It constitutes a reality we must take into consideration in infantile abdominal pathology. A best knowledge of this malformation pattern the present time, allows an early surgical management which leads in almost cases to a definitive recovery