Interobserver Analysis of Albertoni Classification for Mallet Finger, Using Plain Radiography: Importance of the Goniometer / Análise interobservador da classificação das lesões em dedo em martelo segundo Albertoni, utilizando-se radiografias simples: Importância do uso do goniômetro

Abstract Objectives The objective of the present study is to evaluate the intraobserver and interobserver reliability of the Albertoni classification for mallet finger. Evaluation of goniometer device application is also an objective. Methods A total of 10 lateral radiographs of patients with mallet finger were selected and measured by 60 orthopedic surgeons with and without the use of goniometer. Results The intra- and interobserver reliability coefficients found were high. With the use of a goniometer, the interobserver reliability coefficient was even higher, but without statistical relevance. Conclusion The Albertoni classification showed high intraobserver and interobserver reliability in assessing mallet finger lesions, and the goniometer is dispensable for this purpose.

Resumo Objetivos Quantificar o grau de concordância intra- e interobservador da classificação Albertoni e avaliar a importância do uso do goniômetro na diferenciação do grau da lesão. Métodos Foram selecionados 10 casos de dedo em martelo, os quais foram avaliados por 60 examinadores. Resultados A concordância interobservador sem o uso do goniômetro foi elevada. Com o uso do goniômetro, obteve-se um "kappa" ainda maior, porém sem relevância estatística. Conclusão A Classificação de Albertoni possui elevada concordância intra- e interobservador, e o uso do goniômetro se mostrou dispensável para classificar.

Disabilities in leprosy: an open, retrospective analyses of institutional records

Abstract Background and objectives: Leprosy remains a leading cause of peripheral neuropathy and disability in the world. Primary objective of the study was to determine the incidence of deformities present at a time of diagnosis and new deformities that patients develop over follow up period. Material and methods: An open, retrospective cohort study was performed at a tertiary medical center in western India. Recruitment phase of the study was of 2 years (2009-2010) followed by observation/follow up phase of 7 years till 31st December 2017. New patients with leprosy and released from treatment cases who presented with deformity as defined by WHO disability grade (1998) and subsequently developing new deformities during the follow up period of up to 7 years were included in the study. Results: The study included 200 leprosy patients. Of the total 254 deformities, 168 (66.14%) deformities were noticed at the moment of diagnosis, 20 (7.87%) deformities occurred during the follow up phase. Of all patients, 21.25% had Grade 1 deformity and 6.31% had Grade 2 or more severe deformity. Deformities of hand were most common in 44.48%, followed by feet 39.76%, and face 15.74% respectively. Limitation of study: Mode of inclusion of patient was self-reporting during follow up phase so there is possible under reporting of the disabilities. Conclusion: New deformities continue to develop in certain forms of leprosy even after release from treatment. Long-term & regular follow up of patients who have been released from treatment is required.

Colgajo de Atasoy: revisión de una técnica clásica para reconstrucción digital / Atasoy flap: review of a classical technique for digital reconstruction

Resumen Aproximadamente el 50% de las lesiones de mano atendidas en urgencias corresponden a la punta de los dedos, dentro de estas el manejo de las amputaciones requiere una cobertura adecuada, aseguramiento de la sensibilidad táctil, mantención de la longitud y provisión de un lecho de crecimiento y almohadilla para la uña y pulpejo respectivamente; así, con resultados estéticos y funcionales que permitan una incorporación laboral temprana. El presente artículo realiza la descripción de la técnica colgajo de Atasoy o de V en Y, una herramienta que logra las metas reconstructivas en amputaciones dorsales oblicuas o transversas. Lo anterior basados en la literatura, disecciones en cadáveres y casos clínicos. MÉD.UIS. 2018;31(1):57-63.

Abstract Approximately 50% of hand injuries attended in the emergency room correspond to the fingertips, among these the management of amputations requires adequate coverage, ensuring tactile sensitivity, preservation of finger length and provision of a growth bed and pad for the nail and pulp respectively; thus, with esthetic and functional results that allow an early labor incorporation. This article describes the Atasoy or V in Y flap technique, a tool that achieves the reconstructive goals in oblique or transverse dorsal amputations. The above based on the literature, corpse dissections and successful clinical cases. MÉD.UIS. 2018;31(1):57-63.

Evaluation of interobserver agreement in Albertoni's classification for mallet finger / Avaliação de concordância interobservador da classificação de Albertoni para dedo em martelo

ABSTRACT Objective: To measure the reliability of Albertoni's classification for mallet finger. Methods: Agreement study. Forty-three radiographs of patients with mallet finger were assessed by 19 responders (12 hand surgeons and seven residents). Injuries were classified by Albertoni's classification. For agreement comparison, lesions were grouped as: (A) tendon avulsion; (B) avulsion fracture; (C) fracture of the dorsal lip; and (D) physis injury-and subgroups (each group divided into two subgroups). Agreement was assessed by Fleiss's modification for kappa statistics. Results: Agreement was excellent for Group A (k = 0.95 (0.93-0.97)) and remained good when separated into A1 and A2. Group B was moderate (k = 0.42 (0.39-0.44)) and poor when separated into B1 and B2. In the Group C, agreement was good (k = 0.72 (0.70-0.74)), but when separated into C1 and C2, it became moderate. Group D was always poor (k = 0.16 (0.14-0.19)). The general agreement was moderate, with (k = 0.57 (0.56-0.58)). Conclusion: Albertoni's classification evaluated for interobserver agreement is considered a reproducible classification by the method used in the research.

RESUMO Objetivo: Avaliar a reprodutibilidade da classificação de Albertoni para dedo em martelo. Métodos: Foi feita uma avaliação por meio de questionário no qual foram avaliadas 43 radiografias em perfil da articulação interfalângica distal de dedos da mão, com lesão tipo dedo em martelo. Todas as lesões foram caracterizadas pela classificação de Albertoni, por 19 entrevistados (12 cirurgiões de mão e sete residentes). Foi então avaliada a concordância com o coeficiente Kappa generalizado, separadas por grupos - (A) avulsão tendínea; (B) fratura avulsão; (C) fratura do lábio dorsal e (D) lesão fisária - e por subgrupos (cada grupo dividido em 1 e 2). Resultados: A concordância foi excelente para o grupo A (k = 0,95 [0,93-0,97]) e manteve-se boa quando separados em A1 e A2. No grupo B, a concordância foi moderada (k = 0,42 [0,39-0,44]), e foi ruim quando separada em B1 e B2. No grupo C, a concordância foi boa (k = 0,72 [0,70-0,74]), mas quando separada em C1 e C2 se tornou moderada. No grupo D foi sempre ruim (k = 0,16 [0,14-0,19]). A concordância geral foi moderada (k = 0,57 [0,56-0,58]). Conclusão: Pela avaliação da concordância geral, a classificação de Albertoni é considerada reprodutível pelo método usado na pesquisa.

Porfiria cutánea tarda como manifestación extrahepática de hepatitis C crónica: reporte de un caso / Porphyria cutanea tarda as extrahepatic manifestation of chronic hepatitis C: a case report

Se presenta el caso de un paciente varón de 56 años quien es evaluado por presentar a nivel del dorso de ambas manos cicatrices hiperpigmentadas e hipopigmentadas, asociadas a quistes de milia. Se le realizó estudios del metabolismo de las porfirinas y biopsia cutánea de las lesiones los cuales resultaron compatibles con porfiria cutánea tarda. En el laboratorio inicial se encontró elevación de los valores de transaminasas, identificándose posteriormente infección crónica por virus de hepatitis C. Con la finalidad de tratar la infección viral y resolver el compromiso dérmico, considerado como manifestación extrahepática del virus hepatitis C, se inició tratamiento con interferón pegilado y ribavirina evolucionando favorablemente con respuesta viral rápida, carga viral no detectable hasta la actualidad (36 semanas de tratamiento), disminución del nivel de transaminasas séricas y mejoría de las lesiones dérmicas.

The present case is a 56 year old male who present hyperpigmented and hypopigmented scars in both hands, associated with the presence of milia cysts. It was studied the metabolism of porphyrins and skin biopsy of the lesions which were compatible with porphyria cutanea tarda. In the initial laboratory, elevated transaminases values were found and subsequently identified chronic infection of hepatitis C virus. In order to treat viral infection and resolve the dermal commitment; considered extrahepatic manifestation of hepatitis C virus, treatment was started with pegylated interferon and ribavirin, with favorably development and rapid viral response, with undetectable viral load until now (24 weeks of treatment), decreased level of serum transaminases and improvement of skin lesions.

Reconstrução tardia na mão traumatizada com perda de múltiplos dedos / Late reconstruction of a traumatized hand with loss of multiple fingers

As lesões mutilantes de mão são um desafio para o cirurgião de mão e o paciente. O cirurgião deve tomar decisões desde o debridamento inicial, escolhendo quais dedos e articulações serão preservadas e uso apropriado das partes a serem retiradas. A reconstrução tardia é a segunda parte dessa difícil tarefa. Dificuldade que se atribui à particularidade de cada lesão, do grande número de possibilidades de tratamento e seus diversos níveis de complexidade que devem ser adequados à necessidade e motivação pessoal de cada paciente. Este relato de caso apresenta uma reconstrução tardia de mão com perda de indicador e dedo médio com transplante de articulação metacarpofalângica de indicador para função de interfalangeana proximal de dedo médio.

Mutilating hand injuries are a challenge to both the hand surgeon and the patient. The surgeon must make decisions ranging from the initial debridement to which fingers and joints will be preserved and the appropriate use of the parts to be removed. Late reconstruction constitutes the second part of this difficult task. The difficulty attributed to the characteristics of each lesion, the large number of treatment possibilities, and the different levels of complexity must be adapted to the personal needs and motivation of each patient. This case report describes a late hand reconstruction with index and middle finger loss, using metacarpophalangeal joint transplantation of the index finger to gain the proximal interphalangeal function of the middle finger.

Macrodactilia: estudo retrospectivo de quatro casos / Macrodactyly: a retrospective study of four cases

INTRODUÇÃO: A macrodactilia é uma anomalia rara e de etiologia desconhecida. Os primeiros casos foram descritos, em 1821, por Klein. Representa aproximadamente 1% de todas as anomalias congênitas. Surge no nascimento e caracteriza-se pelo crescimento dos dedos das mãos, dos pés ou de todo o membro; entretanto, pode se apresentar mais tardiamente, com os sintomas de compressão de nervo, podendo associar-se à síndrome do túnel do carpo. MÉTODOS: Estudo retrospectivo de quatro casos de macrodactilia atendidos no Hospital da Santa Casa Misericórdia de Campo Grande, MS, nos últimos 10 anos. RESULTADOS: Descrevemos quatro casos de macrodactilia, sendo três em quirodáctilos e um acometendo primeiro pododáctilo. Todos os pacientes tratados com procedimentos cirúrgicos, um dos casos com amputação de falanges e metacarpo. CONCLUSÕES: É recomendada a amputação como opção cirúrgica em alguns casos e o tratamento precoce da síndrome do túnel do carpo quando presente.

INTRODUCTION: Macrodactyly is a rare anomaly of unknown etiology. The first cases were described in 1821 by Klein. It represents approximately 1% of all congenital anomalies. It appears at birth and is characterized by excessive growth of the fingers, toes, or of the entire limb; however, its appearance may be delayed, with symptoms of nerve compression, and may present with carpal tunnel syndrome. METHODS: Retrospective study of four cases of macrodactyly treated at the Hospital da Santa Casa Misericórdia in Campo Grande, MS, in the last 10 years RESULTS: We describe four cases of macrodactyly: three in the fingers and one affecting the first toe. All patients were treated with surgical procedures, one with amputation of phalanges and metacarpals. CONCLUSIONS: Amputation is a surgical option recommended in some cases, as is the early treatment of carpal tunnel syndrome.

Treatment of chronic mallet finger deformity with minor bone anchors and palmaris longus tendon graft / 中国骨伤

<p><b>OBJECTIVE</b>To explore the clinical effects of minor bone anchors and palmaris longus tendon graft in treating chronic mallet fingers deformity.</p><p><b>METHODS</b>From January 2008 to June 2013, 26 patients with chronic mallet fingers deformity were treated with minor bone anchors and palmaris longus tendon graft. There were 18 males and 8 females, aged from 18 to 52 years old with an average of (32.0±1.3) years. Among them, 8 cases caused by machine injury, 6 cases by fall injury, 6 cases by sprain from fight, 4 cases by tendon spontaneous rupture, 2 cases by knife trauma. There was no tendon attachment of extensor tendon check in 16 cases, and with 0.3 to 0.5 cm tendon attachment in 10 cases. All patients had the flexion deformity and the disability of dorsiflexion activity. During operation, the distal interphalangeal joint was fixed in 10° to 20° dorsiflexion by a Kirshner wire, the minor bone anchor was used to reconstruct the extensor tendon insertion, the palmaris longus tendon slice was transplanted the decayed area of extensor tendon insertion. Four weeks postoperatively, the Kirshner wire was removed and the plaster external fixation was used, and the patient began function exercises. Postoperative complications were observed and fingers functions were assessed according to Dargan standard.</p><p><b>RESULTS</b>The patients were followed up from 6 to 14 months with an average of (5.0±0.3) months. Wound superficial infection occurred in 2 cases, the skin pressure ulcer in 2 cases, joint activities disability in 1 case; these symptoms got improvement after symptomatic treatment. Traumatic arthritis occurred in 2 cases, 1 case was improved after treatment, and 1 case had chronic pain for a long time. No internal fixation loosening or breakage and tendon rupture were found. According to Dargan standard to evaluate the finger function, 17 cases got excellent results, 8 good, and 1 poor.</p><p><b>CONCLUSION</b>It is an effective way to treat the chronic mallet finger deformity using minor bone anchors and palmaris longus tendon graft, and the method has advantages of reliable fixation, easy operation, satisfactory effect and less complication.</p>

Mutation c.1190-1delG/N in intron 8 and c.1708G>C/N in exon 12 not reported in the IDUA gene developed a clinical phenotype of Scheie syndrome / Mutación c.1190-1delG/N en el intrón 8 y c.1708G>C/N en el exón 12 no reportada en el gen de IDUA desarrolló un fenotipo clínico de síndrome de Scheie

Mucopolysaccharidoses are a group of lysosomal storage disorders caused by deficiency of enzymes catalyzing the degradation of glycosaminoglycans. Mucopoly-saccharidosis I can present a wide range of phenotypic characteristics with three major recognized clinical entities: Hurler and Scheie syndromes represent phenotypes at the severe and mild ends of the clinical spectrum, respectively, and the Hurler-Scheie syndrome is intermediate in phenotypic expression. These are caused by the deficiency or absence of α-L-iduronidase, essential to the metabolism of both dermatan and heparan sulfate, and it is encoded by the IDUA gene. We report the case of a 34-year-old male patient with enzymatic deficiency of α-L-iduronidase, accumulation of its substrate and a previously unreported mutation in the IDUA gene that developed a phenotype of Scheie syndrome.

Las mucopolisacaridosis son un grupo de trastornos de almacenamiento lisosomal causada por la deficiencia de enzimas que catalizan la degradación de glicosaminoglicanos. La mucopolisacaridosis tipo I puede presentar un amplio rango de características fenotípicas englobadas en tres entidades clínicas reconocidas: los síndromes de Hurler y Scheie representan los fenotipos graves y leves del espectro clínico, respectivamente y el síndrome de Hurler-Scheie intermedio en la expresión fenotípica. Estos son causados por la deficiencia o ausencia de la α-L-iduronidasa esencial para el metabolismo del dermatán y el heparán sulfato y es codificada por el gen IDUA. Se presenta el caso de paciente masculino de 34 años de edad con deficiencia enzimática de α-L-iduronidasa, acumulación de su sustrato y una mutación en el gen IDUA, no reportada previamente, que desarrolló un fenotipo del síndrome de Scheie.

Epidermólise bolhosa distrófica: aspectos dermatológicos e cirúrgicos / Dystrophic epidermolysis bullosa: dermatological and surgical aspects

A epidermólise bolhosa é uma doença hereditária que causa alterações em proteínas estruturais da pele e consequente fragilidade da epiderme. Manifesta-se por surgimento de flictenas por todo o corpo e deformidades funcionais de membros, especialmente nas mãos, sendo que as formas mais características são pseudossindactilia e contraturas. Neste trabalho, descrevemos o caso de um paciente de 12 anos com deformidades nas mãos e flictenas pelo corpo que foi submetido à cirurgia da mão para recuperação da movimentação funcional (AU)

Epidermolysis bullosa is a hereditary disease that causes changes in structural proteins of the skin and consequent fragility of the epidermis. It is manifested by the appearance of blisters all over the body and functional deformities of limbs, especially the hands, and the most characteristic forms are pseudosyndactyly and contractures. In this paper, we describe the case of a 12-year-old patient with deformities in his hands and blisters over the body who underwent hand surgery for recovery of functional movement (AU)

Arthrodesis of Distal Interphalangeal Joints in the Hand with Interosseous Wiring and Intramedullary K-wire Fixation

BACKGROUND: To evaluate the efficacy of intramedullary K-wire fixation and interosseous wiring in the arthrodesis of the distal interphalangeal (DIP) joint with description of surgical procedure. METHODS: We retrospectively analyzed 9 cases (7 women and 2 men) of DIP joint arthrodesis. The average age of patients was 44.2 years (range, 21 to 71 years) and the mean follow-up period was 19.6 months. Joint union was evaluated on the follow-up radiographs together with postoperative complications. RESULTS: All cases achieved radiologic union of the arthrodesis site. There was no surgical complication except for one case of skin irritation by the interosseous wire knot which was removed during the follow-up period. CONCLUSIONS: Intramedullary K-wire fixation and interosseous wiring could be an alternative procedure of arthrodesis in the DIP joint.

Mallet finger deformities treated by buried purse-string suture / 中华创伤杂志(英文版)

<p><b>OBJECTIVE</b>To investigate the efficacy of buried purse-string suture in the treatment of mallet finger deformities.</p><p><b>METHODS</b>From February 2009 to February 2010, 12 patients with closed non-fracture mallet fingers were treated by buried purse-string suture. The rupture tendons were sutured by purse-string suture with an atraumatic needle, and the knots were buried under subcutaneous tissue. External fixator was used at the extension position of the finger every night within three weeks after operation.</p><p><b>RESULTS</b>All patients were followed up for 6-12 months, mean 7 months. According to the Patel's evaluation criteria, 2 cases (17%) obtained excellent results, 7 good (58%), 2 fair (17%) and 1 poor (8%). The overall rate of the cases with excellent and good outcomes was 75%.</p><p><b>CONCLUSION</b>Buried purse-string suture is an easy and effective way to treat mallet finger deformities, with no serious postoperative complications or no need for reoperation.</p>

Correction of claw hand deformity after burns by elastic traction / 中华整形外科杂志

<p><b>OBJECTIVE</b>To investigate a new method for correction of claw hand deformity after burns.</p><p><b>METHODS</b>From May 2006 to Jul. 2010, 12 patients with claw hands deformities after burns were treated with skin grafts (11 hands) and skin flap (1 hand) with unsatisfactory results. Then elastic traction (skin traction or skeletal traction) were performed with individual functional brace.</p><p><b>RESULTS</b>All patients were followed up for 0.5 to 2 years. Elastic traction was effective in the correction of metacarpophalangeal joint deformity, buttonhole deformity, thumb-in-palm deformity, scar contracture, and palmar arch deformity.</p><p><b>CONCLUSIONS</b>Elastic traction is a simple and effective way for the correction of claw hand deformity after burns with less morbidity and stable results.</p>

A importância do diagnóstico precoce da hanseníase na prevenção de incapacidades / The importance of early diagnosis of leprosy in the prevention of disability

A hanseníase é amplamente conhecida por suas complicações neurais e curso desafiador, apesar de rotina terapêutica bem estabelecida. A fim de evitar o desenvolvimento de incapacidades físicas, ressaltamos o papel fundamental do diagnóstico precoce, interrompendo o surgimento de neuropatias hansênicas. Relatamos um caso com evolução para garra ulnar.

Leprosy is well known because it's neural complications and challenging evolution, despite the established treatment. To avoid the development of physical incapacities, we emphasize the fundamental paper of early diagnose, stopping the appearance of leprosy neuropathies. We describe a case with evolution to ulnar claw.

Nosologia das doenças da mão de crianças e jovens operados em mutirões realizados em hospital de referência no estado de pernambuco / Nosology of hand diseases in children and adolescents operated in provisional facilities in a model hospital - pernambuco state, Brazil

OBJETIVO: Relatar a frequência das doenças congênitas da mão operadas em sistema de mutirão no SOS Mão de Recife entre 2005 e 2009. MÉTODOS: Foram coletadas as informações de 833 crianças e adolescentes examinados em oito missões. RESULTADOS: Entre os pacientes, 306 (36,7 por cento) foram operados; 240 (78,4 por cento) por malformações congênitas e 66 (21,6 por cento) por lesões adquiridas. As malformações congênitas mais frequentes foram: sindactilia, 72 (30,0 por cento) casos; polidactilia, 30 (12,5 por cento) casos; polegar bífido, 19 (7,9 por cento) casos; malformação complexa da mão, 14 (5,8 por cento) casos; mão em fenda, 13 (5,4 por cento) casos; dedo em gatilho, 12 (5,0 por cento) casos; camptodactilia, 11 (4,6 por cento) casos; e braquisindactilia, nove (3,7 por cento) casos. As lesões adquiridas mais frequentes foram: lesões por trauma obstétrico, 26 (39,4 por cento) casos; sequela de trauma de mão, 18 (27,3 por cento) casos; sequela de paralisia cerebral, sete (10,6 por cento) casos; sequela de choque elétrico, cinco (7,6 por cento) casos; e sequela de queimadura, quatro (6,1 por cento) casos. CONCLUSÃO: A nosologia das doenças de mão é similar a de grandes séries de cirurgias eletivas, particularmente no que diz respeito às deformidades congênitas. As frequências das lesões adquiridas parecem ser mais altas do que as das séries internacionais. O sistema de mutirão de cirurgia de mão é importante para diminuir a carência dessa atividade em instituições públicas e tem se mostrado muito eficiente. O êxito do projeto pode oferecer subsídio para o Sistema Único de Saúde admitir cirurgiões da mão em sistema de plantão ou sobreaviso nas unidades de emergência.

OBJECTIVE: To report the frequencies of congenital hand diseases in patients who underwent surgery in a provisional clinic as part of the Hand of Recife SOS- Recife, Pernambuco, from 2005 to 2009. METHODS: The information was collected from 833 children and adolescents cared for in eight missions. RESULTS: Among the patients, 306 (36.7 percent) underwent surgery; 240 (78.4 percent) for congenital malformation, and 66 (21.6 percent) for acquired lesions. The most frequent malformations were: syndactyly, 72 (30.0 percent) cases; polydactyly, 30 (12.5 percent) cases; bifid thumb, 19 (7.9 percent) cases; complex hand anomaly, 14 (5.8 percent) cases; cleft hand, 13 (5.4 percent) cases; trigger finger, 12 (5.0 percent) cases; camptodactyly, 11 (4.6 percent) cases; and brachysyndactyly, 9 (3.7 percent) cases. The most frequent acquired injuries were: obstetric brachial plexus paralysis, 26 (39.4 percent) cases; hand trauma sequelae, 18 (27.3 percent) cases; cerebral paralysis sequelae, 7 (10.6 percent) cases; electrical shock sequelae, 5 (7.6 percent) cases; and hand burn injury, 4 (6.1 percent) cases. CONCLUSION: The nosology of hand diseases is, as a whole, similar to the great series of elective hand surgeries, especially regarding congenital hand abnormalities. The frequencies of acquired hand lesions seem to be higher than in the international series. The provisional clinic hand surgery system is important in decreasing the need for this activity in public institutions, and it has been shown to be very effective. The good outcomes of the missions may offer support for The Brazilian Health System to enroll hand surgeons in the on-call system in the emergency units.

Macrodactilia na mão: relato de caso / Hand macrodactyly: a case report

Os autores descrevem a evolução de um caso de macrodactilia digital progressiva na mão ao longo de 10 anos e os programas cirúrgicos e de reabilitação utilizados. Criança do sexo feminino foi admitida no Hospital de Reabilitação aos 10 meses de idade, apresentava macrodactilia digital progressiva no II e III quirodáctilos da mão esquerda. Evoluiu com síndrome do túnel do carpo, atrofia e perda da oponência do polegar. Aos dois anos, foi submetida a amputação do III raio; aos seis anos, a encurtamento do II dedo, epifisiodese e, aos nove anos, a retinaculotomia dos flexores, amputação do II raio e restauração da oponência do polegar com a transferência do extensor próprio do índex. Foram necessários vários procedimentos e métodos de tratamento para o alívio dos sintomas de compressão do nervo mediano e resultado final funcional satisfatório. Os autores recomendam a amputação como opção cirúrgica e o tratamento precoce da síndrome do túnel do carpo.

The authors describe the progress over a ten year period of a single hand macrodactyly digital progressive case and corresponding surgical and rehabilitation procedures used. The female child was first evaluated at the hospital at the age of 10 months, with macrodactyly digital progressive at I and II fingers of the left hand. Afterwards she developed carpal tunnel syndrome, atrophy and lost of thumb opposition. The third ray was amputated at age 2. At age 6 she was realized finger shortening, physeal arrest and at age 9 a carpal tunnel release, II ray resection and proprius extensor tendon opponensplasty. Many interventions and treatment methods were required to relieve the compression symptoms of the median nerve and satisfactory final functional result. The authors recommend amputation as a surgical option and early carpal tunnel release.