Juvenile Hyaline Fibromatosis

Juvenile hyaline fibromatosis (JHF) is a rare, progressive autosomal recessive disease that's characterized by papulonodular skin lesions, soft tissue masses, joint contractures, gingival hypertrophy and osteolytic bone lesions. We present here the case of a 2-yr-old boy with JHF along with a review of the relevant literature. This case demonstrates that JHF should be considered in the differential diagnosis when multiple subcutaneous nodules are observed in the face, head and neck.

Erratum: Correction for incorrectly displaying several words

The publisher wishes to apologize for incorrectly displaying several words. We correct the words from inclu-des (page 104, line 11, right column) to includes, from eventualry (page 105, line 24, left column) to eventually, from approprlate (page 105, line 28, left column) to appropriate, and from Early (page 105, 6 line, right column) to early.

Foreign Body Inclusion Cyst of the Nasal Radix after Augmentation Rhinoplasty

Development of a cystic mass on the nasal dorsum is a very rare complication of aesthetic rhinoplasty. Most reported cases are of mucous cyst and entrapment of the nasal mucosa in the subcutaneous space due to traumatic surgical technique has been suggested as a presumptive pathogenesis. Here, we report a case of dorsal nasal cyst that had a different pathogenesis for cyst formation. A 58-yr-old woman developed a large cystic mass on the nasal radix 30 yr after augmentation rhinoplasty with silicone material. The mass was removed via a direct open approach and the pathology findings revealed a foreign body inclusion cyst associated with silicone. Successful nasal reconstruction was performed with autologous cartilages. Discussion and a brief review of the literature will be focused on the pathophysiology of and treatment options for a postrhinoplasty dorsal cyst.

Reflux Symptom Index(RSI) and Reflux Finding Score(RFS) of Persons Taking Health Checkup and Their Relationship with Gastrofiberscopic Findings / 대한이비인후과학회지

BACKGROUND AND OBJECTIVES: Few studies were performed regarding laryngopharyngeal reflux symptoms and reflux findings in persons taking health checkup. The purpose of this study was to evaluate laryngopharyngeal reflux symptom index (RSI) and reflux finding score (RFS) at a healthcare center and their relationship with gastrofiberscopic findings. SUBJECTS AND METHOD: This study included 157 persons taking healthcare program which contained laryngoscopic examination between February 2006 and June 2006. The data of each patients were collected by questionnaire, fill-up sheets of laryngoscopic findings and a retrospective review of medical record. RESULTS: The male to female ratio was about 4 : 1. The mean age was 47 years. The mean values of RSI and RFS were 2.95 and 3.85. Seven (4.5%) persons had RSI more than 13, and 31 (19.7%) persons had RFS more than 7. On gastrofiberscopy, 23 (14.6%) persons had reflux esophagitis, and their RSI were significantly higher than those who did not have reflux esophagitis, and had frequent gastroesophageal reflux symptoms. In persons with abnormal RSI or RFS, only 29% had reflux esophagitis on gastrofiberscopy. Age was inversely related with RSI and smoking was positively related with RFS. CONCLUSION: We suggest that if a person was found to have abnormally elevated RSI or RFS, a diagnostic evaluation for LPR should be considered irrespective of the presence of reflux esophagitis on gastrofiberscopy. In a person with reflux esophagitis on gastrofiberscopy, he or she showed high RSI without any significant differences in RFS : this may have been because the RSI questionnaire included the gastroesophageal reflux symptom item.

Bell's Palsy associated with Acute Vestibulopathy

Bell's palsy is acute idiopathic peripheral facial nerve palsy which is diagnosed after all the possible causes are ruled out. Several symptoms and signs of polyneuropathy, such as hypesthesia of cranial nerve IX or V, vagal motor weakness, retroauricular pain, and hearing impairment were frequently accompanied with Bell's palsy. However, association of vertigo has been rarely reported, and moreover, associated vestibulopathy was not characterized in detail in those cases. We report a 35 year-old male patient with Bell's palsy accompanying acute peripheral vestibular loss, which eventually evolved to benign paroxysmal positional vertigo.