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Korean Journal of Medicine ; : 708-711, 1997.
Artigo em Coreano | WPRIM | ID: wpr-111783

RESUMO

Dilated cardiomyopaty is a rare occurrence in Hecker muscular dystropy. We report a case of Becken muscular dystrophy in 28 old man who presented with dyspnea, progressive muscle weakness, and dilated cardiomyopathy with severe left ventricular dysfunction which was detected by echocardiograpy. Muscle biopsy demonstrated diffuse degenerated changes consistent with progressive muscular dystropy, His brother has also Becker muscular dystrophy and dilated cardiomyopathy, The patient is on NYHA Class II~III with medical therapy.


Assuntos
Humanos , Biópsia , Cardiomiopatia Dilatada , Dispneia , Debilidade Muscular , Distrofias Musculares , Distrofia Muscular de Duchenne , Irmãos , Disfunção Ventricular Esquerda
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