RESUMO
Peutz-Jeghers syndrome is a hereditary affection with dominant autosomal transmission. The risk of cancerisation is largely higher than that in the general population. Dysplasia is rare. Transformation of the polyposis hamartoma into a site of dysplasia then into adenocarcinoma has been rarely reported. The authors report the case of a 14 year-old patient, having a severe dysplasia on ileal polyposis hamartoma related to the syndrome of Peutz-Jeghers
Assuntos
Humanos , Masculino , Família , Adenocarcinoma , Doenças Genéticas Inatas , HamartomaRESUMO
Sertoli-Leidig cell tumor of the ovary is a rare tumor. It accounts for 0.5 - 1% of all ovarian tumors. Sertoli-Leidig cell tumors are commonly benign and they occur in young women who desire further childrearing. Although, the treatment must be as conservative as possible. For the malign Sertoli-Leidig cell tumor, radical treatment is required. The aim of this work is the analysis of clinical, para-clinical and therapeutic aspects of these tumors