Factor X deficiency--a rare disorder.

Congenital factor X deficiency is a very rare inherited coagulation disorder. The clinical phenotype is of varying bleeding manifestations depending upon the level of factor activity. We describe a one and a half year old patient with severe deficiency (factor level less than 1%) who manifested with only easy bruisability and epistaxis that does not correlate with level of deficiency.

Hereditary coagulation factor X deficiency--a clinico-haematological profile of 5 cases from Varanasi.

Hereditary factor X deficiency is one of the rarest inherited coagulation factor deficiency. We are presenting here clinico-haematological profile and diagnostic approach of five such cases seen by us over a period of eleven years (year 1991-2001).